Unrepaired Tetralogy of Fallot in a 73 year old woman

Among cyanotic congenital heart diseases (CHD) Tetralogy of Fallot (TOF) is the most common, with an incidence of 0.28 cases every 1000 live-births. Despite the excellent prognosis related to early surgical correction, usually performed before the sixth month of age, life expectancy without surgery is dramatically reduced [1] and [2]. According to large observational series, 24% of individuals with an uncorrected TOF die before the age of 10 and only 4% survive above thirties [3] and [4]. Survival to advanced age is extremely rare. In the present manuscript we describe the case of a seventy-three year old woman with uncorrected TOF.