The association of pancreatic cystosis and IPMN in cystic fibrosis: case report and literature review

Maria Gabriella Brizi, Riccardo Manfredi, Guido Costamagna, D Pagliari, A Saviano, ML Serricchio, AA Dal Lago, F Attili

Risultato della ricerca: Contributo in rivistaArticolo in rivista

1 Citazioni (Scopus)

Abstract

Pancreatic cystosis is a rare presentation of cystic fibrosis involving pancreatic gland. To date, only very few cases of pancreatic cystosis have been described in literature. Pancreatic cystosis may begin during the second decade of life and is the rarest presentation of cystic fibrosis. This disease is characterized by the presence of multiloculated cysts without ductal system communication of different sizes in all the pancreatic tissue. Herein, we report a case of a young woman affected by cystic fibrosis that was admitted to our Pancreatic Centre to evaluate a picture of diffuse multiloculated pancreatic cysts. After magnetic resonance imaging (MRI) and endoscopic ultrasound (EUS) assessment, we perform the diagnosis of the concomitant presence of the rare condition of pancreatic cystosis with Branch Duct-Intraductal Papillary Mucinous Neoplasm (BD-IPMN). To our knowledge, this is the first reported case of a cystic fibrosis patient with the combination of pancreatic cystosis and IPMN.
Lingua originaleEnglish
pagine (da-a)5179-5184
Numero di pagine6
RivistaEuropean Review for Medical and Pharmacological Sciences
Volume21
Stato di pubblicazionePubblicato - 2017

Keywords

  • Cystic fibrosis
  • Intraductal papillary mucinous neoplasm (IPMN)
  • Magnetic resonance cholangio-pancreatography (MRCP)
  • Pancreatic cystosis
  • Pancreatic mucinous neoplasm

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