Quantitative muscle strength assessment in duchenne muscular dystrophy: longitudinal study and correlation with functional measures

A Lerario, S Bonfiglio, M Sormani, A Tettamanti, S Marktel, S Napolitano, S Previtali, M Scarlato, M Natali Sora, Eugenio Maria Mercuri, N Bresolin, T Mongini, G Comi, Roberto Gatti, F Ciceri, G Cossu, Y. Torrente

Risultato della ricerca: Contributo in rivistaArticolo in rivista

38 Citazioni (Scopus)

Abstract

The aim of this study was to perform a longitudinal assessment using Quantitative Muscle Testing (QMT) in a cohort of ambulant boys affected by Duchenne muscular dystrophy (DMD) and to correlate the results of QMT with functional measures. This study is to date the most thorough long-term evaluation of QMT in a cohort of DMD patients correlated with other measures, such as the North Star Ambulatory Assessment (NSAA) or three 6-min walk test (6MWT).
Lingua originaleEnglish
pagine (da-a)91-91
Numero di pagine1
RivistaBMC Neurology
Volume12
DOI
Stato di pubblicazionePubblicato - 2012

Keywords

  • Adolescent
  • Child, Preschool
  • Humans
  • Longitudinal Studies
  • Male
  • Muscle Strength
  • Muscle Strength Dynamometer
  • Muscular Dystrophy, Duchenne
  • Physical Examination
  • Reproducibility of Results
  • Sensitivity and Specificity
  • Statistics as Topic
  • Young Adult

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