Post-inflammatory retinal dystrophy in CINCA syndrome.

Donato Rigante, Achille Stabile, Angelo Maria Minnella, Laura Avallone, Lucia Ziccardi, Giulia Bersani, Giovanna Stifano, Adele Compagnone, Benedetto Falsini

Risultato della ricerca: Contributo in rivistaArticolo in rivista

13 Citazioni (Scopus)

Abstract

Right chorioretinitis and bilateral pseudopapilledema were firstly appreciated in a 9-month-old child with neonatal findings of aseptic chronic meningitis, framed in the context of CINCA syndrome at 1 year. Therapeutical response to various combinations of drugs was inconsistent until 7 years, when anakinra was started with immediate clinical and laboratory improvement. A state of severe retinal dystrophy of post-inflammatory origin became evident on funduscopy, optical coherence tomography and visual electrophysiology tests at the age of 10 years, which remained stationary after 1 year of anakinra treatment.
Lingua originaleEnglish
pagine (da-a)389-393
Numero di pagine5
RivistaRheumatology International
Volume2010
DOI
Stato di pubblicazionePubblicato - 2010

Keywords

  • CINCA syndrome
  • Retinopathy

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