Muscle magnetic resonance imaging in congenital myopathies due to ryanodine receptor type 1 gene mutations

  • Andrea Klein
  • , Heinz Jungbluth
  • , Emma Clement
  • , Suzanne Lillis
  • , Stephen Abbs
  • , Pinki Munot
  • , Marika Pane
  • , Elizabeth Wraige
  • , Ulrike Schara
  • , Volker Straub
  • , Eugenio Maria Mercuri
  • , Francesco Muntoni

Risultato della ricerca: Contributo in rivistaArticolo

67 Citazioni (Scopus)

Abstract

To establish the consistency of the previously reported pattern of muscle involvement in a large cohort of patients with molecularly defined ryanodine receptor type 1 (RYR1)-related myopathies, to identify possible additional patterns, and to compare magnetic resonance imaging (MRI) findings with clinical and genetic findings.
Lingua originaleInglese
pagine (da-a)1171-1179
Numero di pagine9
RivistaArchives of Neurology
Volume68
DOI
Stato di pubblicazionePubblicato - 2011

Keywords

  • Adolescent
  • Child
  • Child, Preschool
  • Cohort Studies
  • Genes, Dominant
  • Genes, Recessive
  • Humans
  • Infant
  • Infant, Newborn
  • Magnetic Resonance Imaging
  • Muscle, Skeletal
  • Mutation
  • Myopathies, Structural, Congenital
  • Predictive Value of Tests
  • Ryanodine Receptor Calcium Release Channel
  • Single-Blind Method

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