Markers of myeloproliferative diseases in childhood polycythemia vera and essential thrombocythemia

Luciana Teofili, Fiorina Giona, Maurizio Martini, Tonia Cenci, Francesco Guidi, Lorenza Torti, Giovanna Palumbo, Angela Amendola, Robin Foa, Luigi Maria Larocca

Risultato della ricerca: Contributo in rivistaArticolo in rivista

82 Citazioni (Scopus)

Abstract

Polycythemia vera (PV) and essential thrombocythemia (ET) can present in pediatric age as sporadic or familial diseases. To define the biologic profile of childhood PV and ET, we evaluated specific markers in a cohort of pediatric patients affected by PV and ET, including cases with familial occurrence.
Lingua originaleEnglish
pagine (da-a)1048-1053
Numero di pagine6
RivistaJournal of clinical oncology : official journal of the American Society of Clinical Oncology
Volume25
DOI
Stato di pubblicazionePubblicato - 2007

Keywords

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Biological Markers
  • Child
  • Cohort Studies
  • Erythroid Precursor Cells
  • Female
  • Follow-Up Studies
  • GPI-Linked Proteins
  • Humans
  • Incidence
  • Isoantigens
  • Janus Kinase 2
  • Male
  • Membrane Glycoproteins
  • Middle Aged
  • Mutation
  • Myeloproliferative Disorders
  • Pedigree
  • Polycythemia Vera
  • RNA, Messenger
  • Receptors, Androgen
  • Receptors, Cell Surface
  • Receptors, Erythropoietin
  • Receptors, Thrombopoietin
  • Rome
  • Thrombocythemia, Essential
  • Thrombopoietin
  • Thrombosis
  • Time Factors

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