Large pericardial effusion requiring pericardiocentesis as cardinal sign of macrophage activation syndrome in systemic onset-juvenile idiopathic arthritis

Donato Rigante, Gabriella De Rosa, Barbara Bertoni, Valentina Ansuini, Manuela Pardeo, Ilaria La Torraca, Stefania Gaspari, Achille Stabile

Risultato della ricerca: Contributo in rivistaArticolo in rivista

7 Citazioni (Scopus)

Abstract

We report a case of large pericardial effusion which has been managed with pericardiocentesis as the main presentation feature of a dramatic clinical picture, only retrospectively framed as referred to macrophage activation syndrome in a child with juvenile idiopathic arthritis at its onset. The risk of developing this rare and severe complication should be recognized in various pathological settings of childhood, above all in children displaying systemic signs of juvenile idiopathic arthritis.
Lingua originaleEnglish
pagine (da-a)767-770
Numero di pagine4
RivistaRheumatology International
DOI
Stato di pubblicazionePubblicato - 2007

Keywords

  • juvenile arthritis
  • macrophage activation syndrome
  • pericardiocentesis

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