TY - JOUR
T1 - Expanding the spectrum of "mesenchymal" tumors of the central nervous system
AU - Pizzimenti, Cristina
AU - Gianno, Francesca
AU - Gessi, Marco
PY - 2022
Y1 - 2022
N2 - In this review, we summarize the clinical, histopathological, and molecular features of central nervous system (CNS) tumors with BCOR internal tandem duplication, intracranial mesenchymal tumor with FET/CREB fusion, CNS CIC-rearranged sarcomas and primary intracranial sarcoma DICER1-mutant, now included in the 2021 WHO classification of CNS tumors. Possible relationships between tumors occurring in the CNS and their systemic counterparts are discussed.
AB - In this review, we summarize the clinical, histopathological, and molecular features of central nervous system (CNS) tumors with BCOR internal tandem duplication, intracranial mesenchymal tumor with FET/CREB fusion, CNS CIC-rearranged sarcomas and primary intracranial sarcoma DICER1-mutant, now included in the 2021 WHO classification of CNS tumors. Possible relationships between tumors occurring in the CNS and their systemic counterparts are discussed.
KW - CNS CIC-rearranged sarcomas
KW - CNS tumor with BCOR internal tandem duplication
KW - central nervous system
KW - intracranial mesenchymal tumor with FET/CREB fusion
KW - primary intracranial sarcoma DICER1-mutant
KW - CNS CIC-rearranged sarcomas
KW - CNS tumor with BCOR internal tandem duplication
KW - central nervous system
KW - intracranial mesenchymal tumor with FET/CREB fusion
KW - primary intracranial sarcoma DICER1-mutant
UR - http://hdl.handle.net/10807/275075
U2 - 10.32074/1591-951X-826
DO - 10.32074/1591-951X-826
M3 - Article
SN - 1591-951X
VL - 114
SP - 457
EP - 464
JO - Pathologica
JF - Pathologica
ER -