Diffuse lung disease in neurofibromatosis

Rocco Trisolini*, Vanina Livi, Luigi Lazzari Agli, Marco Patelli

*Autore corrispondente per questo lavoro

Risultato della ricerca: Contributo in rivistaArticolo

Abstract

Prevalence, characteristics and the very existence of neurofibromatosis-associated diffuse lung disease remain unclear, mostly because the few studies that looked at pulmonary involvement in such patients used chest X-ray as diagnostic mean. We report on the clinical, functional and HRCT findings in a patient with neurofibromatosis-associated diffuse lung disease and provide a short literature review.
Lingua originaleInglese
pagine (da-a)249-250
Numero di pagine2
RivistaLung
Volume190
Numero di pubblicazione2
DOI
Stato di pubblicazionePubblicato - 2012

All Science Journal Classification (ASJC) codes

  • Medicina Polmonare e Respiratoria

Keywords

  • Diffuse lung disease
  • High-resolution computed tomography
  • Neurofibromatosis
  • Pulmonary fibrosis

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