Association between familial mediterranean fever and retroperitoneal fibrosis: retroperitoneal fibrosis regression after colchicine therapy

Giuliana De Socio, Claudia Cerquaglia, Valentina Curigliano, Claudia Fonnesu, Maria Giovinale, Elisa Carla Bianca Verrecchia, Gme Marino, Luigi Natale, Gb Gasbarrini, Raffaele Manna*

*Autore corrispondente per questo lavoro

Risultato della ricerca: Contributo in rivistaArticolo

9 Citazioni (Scopus)

Abstract

Retroperitoneal fibrosis (RPF) is a disease characterized by inflammatory fibrotic processes affecting the retroperitoneal structures. Familial Mediterranean Fever (FMF) is an autosomal recessive disorder, characterized by fever and attacks of sterile serositis. Colchicine is the only suitable drug for prevention of acute episodes. We describe a case of association between RPF and FMF in a 48-year-old male, in whom therapy with colchicine, besides preventing acute episodes, allowed RPF regression. To date the association between FMF and RPF and the use of colchicine therapy alone for RPF has not been described.
Lingua originaleInglese
pagine (da-a)521-524
Numero di pagine4
RivistaInternational Journal of Immunopathology and Pharmacology
Volume22
Numero di pubblicazione2
DOI
Stato di pubblicazionePubblicato - 2009

All Science Journal Classification (ASJC) codes

  • Immunologia e Allergia
  • Immunologia
  • Farmacologia

Keywords

  • Colchicine
  • Familial Mediterranean Fever
  • Humans
  • Male
  • Middle Aged
  • Remission Induction
  • Retroperitoneal Fibrosis
  • Tomography
  • Treatment Outcome
  • X-Ray Computed

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