Résections hépatiques pour lithiases sur dilatations congénitales des voies biliaires intrahépatiques

[Autom. eng. transl.] OBJECTIVE: This study reports clinical experience with liver resections for congenital dilatation of the bile ducts and associated intrahepatic lithiasis to evaluate outcomes and define indications for treatment. PATIENTS AND METHODS: We studied the clinical data of patients undergoing liver resection from January 1992 to December 2008 and assessed the immediate results at a distance from the interventions. Results.- Of 49 patients treated, 47 underwent liver resection. In the majority of cases the disease was limited to the left liver and left hepatectomy was the most common surgical procedure. Operative mortality was nil and morbidity 24.5%. A cholangiocarcinoma was diagnosed in six cases (12.2%). In 91.6% of cases, the distance results were good or satisfactory. Conclusion.- The objectives of the treatment should be in all cases the elimination of stones, the prevention of recurrence as well as that of cholangiocarcinoma. The excisional surgery represents the best possible treatment for symptomatic patients with localized disease and atrophy of the affected liver.