Post-inflammatory retinal dystrophy in CINCA syndrome.

Donato Rigante; Achille Stabile; Angelo Maria Minnella; Laura Avallone; Lucia Ziccardi; Giulia Bersani; Giovanna Stifano; Adele Compagnone; Benedetto Falsini

doi:10.1007/s00296-009-0939-y

Post-inflammatory retinal dystrophy in CINCA syndrome.

Donato Rigante
, Achille Stabile
, Angelo Maria Minnella
, Laura Avallone
, Lucia Ziccardi
, Giulia Bersani
, Giovanna Stifano
, Adele Compagnone
, Benedetto Falsini

Research output: Contribution to journal › Article

13 Citations (Scopus)

Abstract

Right chorioretinitis and bilateral pseudopapilledema were firstly appreciated in a 9-month-old child with neonatal findings of aseptic chronic meningitis, framed in the context of CINCA syndrome at 1 year. Therapeutical response to various combinations of drugs was inconsistent until 7 years, when anakinra was started with immediate clinical and laboratory improvement. A state of severe retinal dystrophy of post-inflammatory origin became evident on funduscopy, optical coherence tomography and visual electrophysiology tests at the age of 10 years, which remained stationary after 1 year of anakinra treatment.

Original language	English
Pages (from-to)	389-393
Number of pages	5
Journal	Rheumatology International
Volume	2010
DOIs	https://doi.org/10.1007/s00296-009-0939-y
Publication status	Published - 2010

Keywords

CINCA syndrome
Retinopathy

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10.1007/s00296-009-0939-y

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title = "Post-inflammatory retinal dystrophy in CINCA syndrome.",

abstract = "Right chorioretinitis and bilateral pseudopapilledema were firstly appreciated in a 9-month-old child with neonatal findings of aseptic chronic meningitis, framed in the context of CINCA syndrome at 1 year. Therapeutical response to various combinations of drugs was inconsistent until 7 years, when anakinra was started with immediate clinical and laboratory improvement. A state of severe retinal dystrophy of post-inflammatory origin became evident on funduscopy, optical coherence tomography and visual electrophysiology tests at the age of 10 years, which remained stationary after 1 year of anakinra treatment.",

keywords = "CINCA syndrome, Retinopathy, CINCA syndrome, Retinopathy",

author = "Donato Rigante and Achille Stabile and Minnella, \{Angelo Maria\} and Laura Avallone and Lucia Ziccardi and Giulia Bersani and Giovanna Stifano and Adele Compagnone and Benedetto Falsini",

year = "2010",

doi = "10.1007/s00296-009-0939-y",

language = "English",

volume = "2010",

pages = "389--393",

journal = "Rheumatology International",

issn = "0172-8172",

publisher = "Springer Science and Business Media Deutschland GmbH",

}

TY - JOUR

T1 - Post-inflammatory retinal dystrophy in CINCA syndrome.

AU - Rigante, Donato

AU - Stabile, Achille

AU - Minnella, Angelo Maria

AU - Avallone, Laura

AU - Ziccardi, Lucia

AU - Bersani, Giulia

AU - Stifano, Giovanna

AU - Compagnone, Adele

AU - Falsini, Benedetto

PY - 2010

Y1 - 2010

N2 - Right chorioretinitis and bilateral pseudopapilledema were firstly appreciated in a 9-month-old child with neonatal findings of aseptic chronic meningitis, framed in the context of CINCA syndrome at 1 year. Therapeutical response to various combinations of drugs was inconsistent until 7 years, when anakinra was started with immediate clinical and laboratory improvement. A state of severe retinal dystrophy of post-inflammatory origin became evident on funduscopy, optical coherence tomography and visual electrophysiology tests at the age of 10 years, which remained stationary after 1 year of anakinra treatment.

AB - Right chorioretinitis and bilateral pseudopapilledema were firstly appreciated in a 9-month-old child with neonatal findings of aseptic chronic meningitis, framed in the context of CINCA syndrome at 1 year. Therapeutical response to various combinations of drugs was inconsistent until 7 years, when anakinra was started with immediate clinical and laboratory improvement. A state of severe retinal dystrophy of post-inflammatory origin became evident on funduscopy, optical coherence tomography and visual electrophysiology tests at the age of 10 years, which remained stationary after 1 year of anakinra treatment.

KW - CINCA syndrome

KW - Retinopathy

KW - CINCA syndrome

KW - Retinopathy

UR - http://hdl.handle.net/10807/3682

U2 - 10.1007/s00296-009-0939-y

DO - 10.1007/s00296-009-0939-y

M3 - Article

SN - 0172-8172

VL - 2010

SP - 389

EP - 393

JO - Rheumatology International

JF - Rheumatology International

ER -

Post-inflammatory retinal dystrophy in CINCA syndrome.

Abstract

Keywords

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