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'Pathognomonic' muscle imaging findings in DNAJB6 mutated LGMD1D

  • S. M. Sandell
  • , I. Mahjneh
  • , J. Palmio
  • , G. Tasca
  • , Giorgio Tasca
  • , Enzo Ricci
  • , B. A. Udd
  • Seinajoki Central Hospital
  • Pietarsaari Hospital
  • Tampere University
  • IRCCS Fondazione Don Carlo Gnocchi - Milano

Research output: Contribution to journalArticle

Abstract

We have previously reported clinical, genetic and molecular pathomechanistic findings in DNAJB6 mutated LGMD1D. After publishing clinical findings of the original Finnish family we identified more Finnish, Italian and US families with the same disease, ultimately confirmed by mutations in the same gene.
Original languageEnglish
Pages (from-to)1553-1559
Number of pages7
JournalEuropean Journal of Neurology
Volume20
DOIs
Publication statusPublished - 2013

Keywords

  • Adult
  • Aged
  • DNAJB6 myopathy
  • Female
  • Finland
  • HSP40 Heat-Shock Proteins
  • Humans
  • LGMD
  • LGMD1D
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Molecular Chaperones
  • Muscle, Skeletal
  • Muscular Dystrophies, Limb-Girdle
  • Nerve Tissue Proteins
  • Pedigree
  • autosomal dominant LGMD
  • limb-girdle muscular dystrophy

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